LHERMITTE-DUCLOS DISEASE (DYSPLASTIC CEREBELLAR GANGLIOCYTOMA) IN A YOUNG PATIENT – A RARE CASE REPORT

Abstract

Lhermitte - Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar neoplasm. It usually presents with raised intracranial pressure along with cerebellar signs. We report a rare case of Lhermitte - Duclos disease of a 20 years male who presented with signs & symptoms of raised intracranial tension. CT features were suggestive of Lhermitte-Duclos disease. Subtotal excision of the mass followed by histopathological evaluation confirmed the diagnosis. This case has been reported to emphasize clinical presentation and radiological features of this rare entity.

KEYWORDS: Lhermitte -Duclos disease, Dysplastic cerebellar gangliocytoma, Imaging features.