OSTEOPOIKILOSIS: AN INCIDENTAL FINDING IN A PATIENT WITH OLECRANON FRACTURE

Abstract

Osteopoikilosis (osteopathia condensans disseminate, spotted bone; OPK) is a rare bone dysplasia. The skeletal changes of osteopoikilosis were first described by Stieda in 1905 followed by Albers-Schoenberg (1915). It has an autosomal dominant inheritance, and can be observed equally in both sexes and in all age groups. It is an uncommon disorder with an estimated incidence of 1/50,000.1 The etiology and pathogenesis remain unclear. It is usually asymptomatic and is a coincidental finding at radiographic examination. However, mild joint pain and swelling may be seen in 15–20% of cases. The most common localization of these lesions is in the phalanges of the hand, carpal bones, metacarpals, metatarsals, foot phalanges, pelvis, femur and humerus,. There is no involvement of the clavicles, ribs or skull, typical of osteopoikilosis. In the affected bone these lesion are seen in the epiphysis and metaphysis. These multiple, sclerotic, roundish lesions vary in size from a few millimeters to several centimeters.