A CASE REPORT OF SUBEPENDYMAL GIANT CELL ASTROCYTOMA IN 7 MONTH OLD PATIENT WITH TUBEROUS SCLEROSIS

Abstract

Tuberous sclerosis is a neurocutaneous syndrome with a wide variety of clinical, pathologic, and radiologic manifestations. Intracranial phakomatosis has been reported to include subependymal nodules; cortical, and subependymal giant-cell astrocytomas. Subependymal giant-cell astrocytomas are rare, benign typically slow growing tumors of mixed neuroglial lineage, which can become aggressive and cause increased intracranial pressure, seizures, and focal neurologic signs. The standard treatment of these tumors is total neurosurgical resection [1,2,3]. We report a 07 month old male patient with tuberous sclerosis who underwent surgery for a large subependymal giant-cell astrocytoma (SEGA). It is rare to find SEGA in this age period.

Keywords : Subependymal giant-cell astrocytoma(SEGAs); Subependymal nodules (SENs): Tuberous sclerosis(TS)