POLAND SYNDROME: A RARE CASE

Authors

  • CHHABI . INSTITUTE OF POSTGRADUATE MEDICAL EDUCATION AND RESEARCH, KOLKATA
  • BHASKAR BHATTACHARYYA BANGUR INSTITUTE OF NEUROSCIENCES
  • TAPAN DHIBAR BANGUR INSTITUTE OF NEUROSCIENCES

Abstract

Poland syndrome is a rare congenital anomaly characterised by unilateral absence of sternocostal head of pectoralis major muscle and pectoralis minor muscle along with ipsilateral rib anomaly and frequent association with ipsilateral upper limb brachysyndactyly. We present a case of a 10 month old male child having depressed left side of anterior chest wall without respiratory distress. The imaging findings were characteristic and diagnostic of Poland syndrome.

 

Author Biographies

CHHABI ., INSTITUTE OF POSTGRADUATE MEDICAL EDUCATION AND RESEARCH, KOLKATA

JUNIOR RESIDENT

BHASKAR BHATTACHARYYA, BANGUR INSTITUTE OF NEUROSCIENCES

ASSOCIATE PROFESSOR

TAPAN DHIBAR, BANGUR INSTITUTE OF NEUROSCIENCES

PROFESSOR

References

Samuels TH, Haider MA, Kirkbride P. Poland's syndrome: a mammographic presentation. AJR Am J Roentgenol. 1996;166 (2): 347-8.

Fraser FC, Teebi AS, Walsh S, Pinky L. Poland sequence with dextrocardia: Which comes first? Am J Med Genet. 1997;73:194–6.

Fokin AA, Robicsek F. Poland's syndrome revisited. Ann Thorac Surg. 2002;74:2218–25.

Lacorte D, Marsella M, Guerrini P. A case of Poland Syndrome associated with dextroposition. Ital J Pediatr. 2010;36:21.

Pisteljić DT, Vranjesević D, Apostolski S et-al. Poland syndrome associated with 'morning glory' syndrome (coloboma of the optic disc). J. Med. Genet. 1986;23 (4): 364-6.

Becker DW, Jr, Darian, et al. Familial Poland's syndrome – Case No. 15. Ann Plast Surg. 1990;25:74.

Bavinck JN, Weaver DD. Subclavian artery supply disruption sequence: Hypothesis of a vascular etiology for Poland, Klippel-Feil, and Möbius anomalies. Am J Med Genet. 1986;23:903–18.

Ferraro GA, Perrotta A, Rossano F, D’Andrea F. Poland syndrome: Description of an atypical variant. Aesthetic Plast Surg. 2005;29:32–3.

Seyfer AE, Fox JP, Hamilton CG. Poland syndrome: Evaluation and treatment of the chest wall in 63 patients. Plast Reconstr Surg. 2010;126:902–11.

Downloads

Published

20-10-2017

How to Cite

., C., BHATTACHARYYA, B., & DHIBAR, T. (2017). POLAND SYNDROME: A RARE CASE. Pakistan Journal of Radiology, 27(4). Retrieved from https://www.pakjr.com/index.php/PJR/article/view/741

Issue

Section

Case Reports