Imaging Evaluation Of An Extremely Rare Primitive Neuroectodermal Tumor Of Adrenal Gland: An Interesting Case Report
Abstract
Primitive neuroectodermal tumor of adrenal gland is a rare malignant neoplasm. It is categorised under peripheral primitive neuroectodermal tumors (pPNET). They have aggressive course with very poor prognosis. A 10-year-old male patient was being evaluated for left loin pain. Ultrasonography showed a large mass in left lumber region with heterogenous echotexture and increased vascularity on colour Doppler. Computed tomography showed the mass was arising from left suprarenal gland. PET-CT scan revealed the mass was metabolically active. Biopsy from that mass showed histopathological features consistent with primitive neuroectodermal tumor of adrenal originReferences
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